{"id":7277,"date":"2025-09-23T22:24:26","date_gmt":"2025-09-23T22:24:26","guid":{"rendered":"https:\/\/atlasemhematologia.com.br\/?p=7277"},"modified":"2025-09-23T22:24:26","modified_gmt":"2025-09-23T22:24:26","slug":"anemia-hemolitica-microangiopatica","status":"publish","type":"post","link":"https:\/\/atlasemhematologia.com.br\/blog\/anemia-hemolitica-microangiopatica\/","title":{"rendered":"Anemia hemol\u00edtica microangiop\u00e1tica"},"content":{"rendered":"\n<p>A Anemia Hemol\u00edtica Microangiop\u00e1tica (AHM) torna-se um cap\u00edtulo complexo no campo das doen\u00e7as hematol\u00f3gicas. Nessa condi\u00e7\u00e3o, um turbilh\u00e3o de eventos coloca as hem\u00e1cias, respons\u00e1veis pelo transporte vital de oxig\u00eanio, no centro, levando \u00e0 sua destrui\u00e7\u00e3o e desencadeando manifesta\u00e7\u00f5es cl\u00ednicas distintas.<\/p>\n\n\n\n<h4 class=\"wp-block-heading\">Conceito e causas<\/h4>\n\n\n\n<p>Ao desvendar o nome da Anemia Hemol\u00edtica Microangiop\u00e1tica, percebe-se sua natureza: &#8220;Hemol\u00edtica&#8221; e &#8220;microangiop\u00e1tica&#8221;, que indicam, respectivamente, a destrui\u00e7\u00e3o de hem\u00e1cias e a ocorr\u00eancia em vasos de pequeno calibre. Trata-se de uma anemia desencadeada por hem\u00f3lise em capilares, frequentemente desencadeada pela deposi\u00e7\u00e3o de fibrina ou dano endotelial.<\/p>\n\n\n\n<div class=\"wp-block-image\"><figure class=\"aligncenter size-large is-resized\"><img fetchpriority=\"high\" decoding=\"async\" src=\"https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2024\/01\/anemia_hemolitica.jpg\" alt=\"\" class=\"wp-image-7279\" width=\"272\" height=\"280\"\/><figcaption>Representa\u00e7\u00e3o 3D de hem\u00e1cias normais e danificadas. Cr\u00e9dito: Farm\u00e1cia Sa\u00fade.<\/figcaption><\/figure><\/div>\n\n\n\n<p>A causa subjacente \u00e9 diversificada, mas todas as etiologias s\u00e3o graves e demandam abordagens terap\u00eauticas espec\u00edficas. Entre as principais causas, destacam-se a P\u00farpura Trombocitop\u00eanica Tromb\u00f3tica (PTT), Coagula\u00e7\u00e3o Intravascular Disseminada (CIVD), S\u00edndrome de Help, ecl\u00e2mpsia, hipertens\u00e3o arterial maligna e a s\u00edndrome hemol\u00edtica ur\u00eamica (SHU).<\/p>\n\n\n\n<div class=\"wp-block-image\"><figure class=\"aligncenter size-large is-resized\"><img decoding=\"async\" src=\"https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2024\/01\/photo1680191466.jpeg\" alt=\"\" class=\"wp-image-7282\" width=\"398\" height=\"271\"\/><figcaption>L\u00e2mina de paciente com PTT. Cr\u00e9dito: membro do Time Atlas.<\/figcaption><\/figure><\/div>\n\n\n\n<h4 class=\"wp-block-heading\">Patog\u00eanese<\/h4>\n\n\n\n<p>Na PTT, a a\u00e7\u00e3o crucial da enzima ADAMTS13 \u00e9 evidente; sua defici\u00eancia, seja funcional ou quantitativa, pode resultar na n\u00e3o clivagem de mult\u00edmeros de fator de Von Willebrand. Esse cen\u00e1rio propicia a agrega\u00e7\u00e3o plaquet\u00e1ria antecipada, formando obst\u00e1culos ao fluxo sangu\u00edneo e conduzindo \u00e0 fragmenta\u00e7\u00e3o das hem\u00e1cias. <\/p>\n\n\n\n<div class=\"wp-block-image\"><figure class=\"aligncenter size-large is-resized\"><img decoding=\"async\" src=\"https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2024\/01\/Pathogenesis-of-idiopathic-TTP-caused-by-ADAMTS13-deficiency-Multimeric-VWF-adheres-to.png\" alt=\"\" class=\"wp-image-7280\" width=\"366\" height=\"314\"\/><figcaption>Mecanismo da ADAMTS13. Cr\u00e9dito: ResearchGate.<\/figcaption><\/figure><\/div>\n\n\n\n<p>J\u00e1 a SHU, frequentemente associada a infec\u00e7\u00f5es, especialmente Escherichia coli, apresenta uma toxina shiga-s\u00edmile que desencadeia uma cascata inflamat\u00f3ria nos rins. Isso resulta em les\u00f5es nos vasos, ativa\u00e7\u00e3o do processo de coagula\u00e7\u00e3o e, por conseguinte, hem\u00f3lise.<\/p>\n\n\n\n<h4 class=\"wp-block-heading\">Achados cl\u00ednicos e morfologia<\/h4>\n\n\n\n<p>A distin\u00e7\u00e3o entre PTT e SHU pode apresentar desafios; em ambos os casos, observa-se a presen\u00e7a de esquiz\u00f3citos no esfrega\u00e7o. Dist\u00farbios neurol\u00f3gicos s\u00e3o mais prevalentes na PTT, enquanto a caracter\u00edstica distintiva da SHU \u00e9 a presen\u00e7a de insufici\u00eancia renal.<\/p>\n\n\n\n<h4 class=\"wp-block-heading\">Diagn\u00f3stico e tratamento<\/h4>\n\n\n\n<p>A an\u00e1lise do esfrega\u00e7o e a observa\u00e7\u00e3o das manifesta\u00e7\u00f5es cl\u00ednicas s\u00e3o fundamentais para o diagn\u00f3stico. A plasmaf\u00e9rese \u00e9 uma abordagem terap\u00eautica comum, removendo subst\u00e2ncias t\u00f3xicas e anticorpos patog\u00eanicos. No caso da SHU, o eculizumabe, um anticorpo monoclonal, surge como uma interven\u00e7\u00e3o promissora, visando neutralizar a prote\u00edna C5 do Sistema Complemento.<\/p>\n\n\n\n<div class=\"wp-block-image\"><figure class=\"aligncenter size-large is-resized\"><img loading=\"lazy\" decoding=\"async\" src=\"https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2024\/01\/Alerta_Anvisa_identifica_lote_falsificado_do_medicamento_Soliris.jpg\" alt=\"\" class=\"wp-image-7281\" width=\"413\" height=\"274\"\/><figcaption>Medicamento usado no tratamento da SHU. Cr\u00e9dito: ICTQ.<\/figcaption><\/figure><\/div>\n\n\n\n<h4 class=\"wp-block-heading\">Refer\u00eancias<\/h4>\n\n\n\n<ol class=\"wp-block-list\"><li>MELO, M. A. W.; SILVEIRA, C. M. Laborat\u00f3rio de Hematologia \u2013 Teorias, T\u00e9cnicas e Atlas. 1\u00b0 ed. R\u00fabio. 288p. 2015.&nbsp;<\/li><li>Bain, Barbara J. C\u00e9lulas sangu\u00edneas : um guia pr\u00e1tico [recurso eletr\u00f4nico] \/ BarbaraJ. Bain ; [tradu\u00e7\u00e3o: Renato Failace]. \u2013 5. ed. \u2013 Porto Alegre : Artmed, 2016.<\/li><li>CI\u00caNCIA NEWS. Dispon\u00edvel em: <a href=\"https:\/\/www.ciencianews.com.br\/arquivos\/ACET\/IMAGENS\/revista_virtual\/hematologia\/hemato22.pdf\">https:\/\/www.ciencianews.com.br\/arquivos\/ACET\/IMAGENS\/revista_virtual\/hematologia\/hemato22.pdf<\/a>. Acesso em: 04 de janeiro de 2024.&nbsp;<\/li><li>FAILACE. R.; FERNANDES, F. Hemograma: Manual de interpreta\u00e7\u00e3o. 6\u00b0 ed. Artmed. 2015.&nbsp;<\/li><li>ZAGO. M. A.; FALC\u00c3O, R. P.; PASQUINI, R. Tratado de Hematologia. Atheneu. p.899. 2013.&nbsp;<\/li><li>MEDCURSOS (Medgrupo). Volume 2. Anemias parte 2. 2017.<\/li><\/ol>\n","protected":false},"excerpt":{"rendered":"<p>A Anemia Hemol\u00edtica Microangiop\u00e1tica (AHM) torna-se um cap\u00edtulo complexo no campo das doen\u00e7as hematol\u00f3gicas. Nessa condi\u00e7\u00e3o, um turbilh\u00e3o de eventos coloca as hem\u00e1cias, respons\u00e1veis pelo transporte vital de oxig\u00eanio, no centro, levando \u00e0 sua destrui\u00e7\u00e3o e desencadeando manifesta\u00e7\u00f5es cl\u00ednicas distintas. Conceito e causas Ao desvendar o nome da Anemia Hemol\u00edtica Microangiop\u00e1tica, percebe-se sua natureza: &#8220;Hemol\u00edtica&#8221; [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":7278,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"pagelayer_contact_templates":[],"_pagelayer_content":"","footnotes":""},"categories":[5],"tags":[],"class_list":["post-7277","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-sem-categoria"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.2 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Anemia hemol\u00edtica microangiop\u00e1tica - Blog - Atlas em Hematologia<\/title>\n<meta name=\"description\" content=\"A Anemia Hemol\u00edtica Microangiop\u00e1tica (AHM) torna-se um cap\u00edtulo complexo no campo das doen\u00e7as hematol\u00f3gicas. 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