{"id":17515,"date":"2026-05-01T12:23:22","date_gmt":"2026-05-01T12:23:22","guid":{"rendered":"https:\/\/atlasemhematologia.com.br\/blog\/?p=17515"},"modified":"2026-04-30T12:25:13","modified_gmt":"2026-04-30T12:25:13","slug":"leucemia-mieloide-cronica","status":"publish","type":"post","link":"https:\/\/atlasemhematologia.com.br\/blog\/leucemia-mieloide-cronica\/","title":{"rendered":"Leucemia Mieloide Cr\u00f4nica"},"content":{"rendered":"\n<p class=\"wp-block-paragraph\">A leucemia mieloide cr\u00f4nica (LMC) \u00e9 classificada como uma neoplasia mieloproliferativa e acomete principalmente adultos, com maior incid\u00eancia entre os 40 e 50 anos. Trata-se de uma doen\u00e7a hematopoi\u00e9tica clonal caracterizada por uma altera\u00e7\u00e3o citogen\u00e9tica espec\u00edfica, resultante da transloca\u00e7\u00e3o cromoss\u00f4mica t(9;22)(q34;q11), conhecida como cromossomo Philadelphia. Essa transloca\u00e7\u00e3o origina o gene de fus\u00e3o <strong>BCR-ABL1<\/strong>, respons\u00e1vel pela produ\u00e7\u00e3o de uma tirosina quinase constitutivamente ativa, que promove prolifera\u00e7\u00e3o celular descontrolada da linhagem mieloide.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Devido \u00e0 evolu\u00e7\u00e3o lenta e muitas vezes assintom\u00e1tica, o diagn\u00f3stico da LMC frequentemente ocorre de forma incidental, durante exames laboratoriais de rotina. Nesse contexto, o hemograma assume papel central como ferramenta de triagem e monitoramento da doen\u00e7a.<\/p>\n\n\n\n<figure class=\"wp-block-image size-full\"><img fetchpriority=\"high\" decoding=\"async\" width=\"758\" height=\"639\" src=\"https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2026\/04\/image-11.png\" alt=\"\" class=\"wp-image-17516\" srcset=\"https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2026\/04\/image-11.png 758w, https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2026\/04\/image-11-300x253.png 300w\" sizes=\"(max-width: 758px) 100vw, 758px\" \/><\/figure>\n\n\n\n<hr class=\"wp-block-separator has-alpha-channel-opacity\"\/>\n\n\n\n<h3 class=\"wp-block-heading\"><strong>1. Aspectos cl\u00ednicos e altera\u00e7\u00f5es hematol\u00f3gicas iniciais<\/strong><\/h3>\n\n\n\n<p class=\"wp-block-paragraph\">A evolu\u00e7\u00e3o cl\u00ednica da leucemia mieloide cr\u00f4nica \u00e9 geralmente insidiosa, podendo permanecer assintom\u00e1tica por longos per\u00edodos. Quando presentes, os sinais e sintomas mais comuns incluem fadiga, perda de peso e esplenomegalia.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">No \u00e2mbito laboratorial, a principal altera\u00e7\u00e3o observada no hemograma \u00e9 a leucocitose com desvio \u00e0 esquerda, caracterizada pela presen\u00e7a de c\u00e9lulas granuloc\u00edticas em diferentes est\u00e1gios de matura\u00e7\u00e3o, desde formas jovens at\u00e9 c\u00e9lulas mais maduras. Esse achado reflete a expans\u00e3o clonal da linhagem mieloide na medula \u00f3ssea e sua libera\u00e7\u00e3o para o sangue perif\u00e9rico.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Al\u00e9m disso, outros achados laboratoriais relevantes podem incluir:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Basofilia e eosinofilia<\/strong>, frequentemente associadas \u00e0 progress\u00e3o da doen\u00e7a<\/li>\n\n\n\n<li><strong>Plaquetose<\/strong>, com contagem de plaquetas superior a 600 \u00d7 10\u00b3\/mm\u00b3<\/li>\n\n\n\n<li><strong>Anemia normoc\u00edtica e normocr\u00f4mica<\/strong>, decorrente da supress\u00e3o da eritropoiese<\/li>\n<\/ul>\n\n\n\n<p class=\"wp-block-paragraph\">Portanto, a an\u00e1lise criteriosa do hemograma \u00e9 fundamental para levantar a suspeita diagn\u00f3stica e direcionar investiga\u00e7\u00f5es complementares.<\/p>\n\n\n\n<hr class=\"wp-block-separator has-alpha-channel-opacity\"\/>\n\n\n\n<h3 class=\"wp-block-heading\"><strong>2. Diagn\u00f3stico citogen\u00e9tico e molecular da LMC<\/strong><\/h3>\n\n\n\n<p class=\"wp-block-paragraph\">O diagn\u00f3stico definitivo da leucemia mieloide cr\u00f4nica baseia-se na identifica\u00e7\u00e3o do cromossomo Philadelphia e do gene de fus\u00e3o <strong>BCR-ABL1<\/strong>. O avan\u00e7o das t\u00e9cnicas laboratoriais permitiu o desenvolvimento de m\u00e9todos altamente sens\u00edveis e espec\u00edficos para detectar essas altera\u00e7\u00f5es gen\u00e9ticas.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Atualmente, exames citogen\u00e9ticos e moleculares s\u00e3o considerados padr\u00e3o ouro para confirma\u00e7\u00e3o diagn\u00f3stica e monitoramento da resposta terap\u00eautica. Essas t\u00e9cnicas possibilitam quantificar a carga molecular da doen\u00e7a e avaliar a efic\u00e1cia do tratamento ao longo do tempo.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Assim, a integra\u00e7\u00e3o entre dados cl\u00ednicos, hematol\u00f3gicos e moleculares \u00e9 essencial para estabelecer o diagn\u00f3stico precoce e definir o progn\u00f3stico dos pacientes com LMC.<\/p>\n\n\n\n<hr class=\"wp-block-separator has-alpha-channel-opacity\"\/>\n\n\n\n<h3 class=\"wp-block-heading\"><strong>3. Fases evolutivas da doen\u00e7a e import\u00e2ncia do monitoramento laboratorial<\/strong><\/h3>\n\n\n\n<p class=\"wp-block-paragraph\">A leucemia mieloide cr\u00f4nica apresenta evolu\u00e7\u00e3o cl\u00ednica dividida em fases distintas, sendo a fase cr\u00f4nica a mais comum no momento do diagn\u00f3stico. Entretanto, alguns pacientes podem evoluir para fases mais avan\u00e7adas, como a fase acelerada e a crise bl\u00e1stica.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">A progress\u00e3o da doen\u00e7a est\u00e1 associada ao agravamento das altera\u00e7\u00f5es laboratoriais e cl\u00ednicas. Um dos principais crit\u00e9rios para identifica\u00e7\u00e3o da crise bl\u00e1stica \u00e9 o aumento significativo da contagem de blastos no sangue perif\u00e9rico ou na medula \u00f3ssea. Esse achado indica transforma\u00e7\u00e3o da doen\u00e7a para uma forma mais agressiva, semelhante a uma leucemia aguda.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Nesse contexto, a morfologia celular e a imunofenotipagem desempenham papel fundamental no acompanhamento da doen\u00e7a, permitindo avaliar a evolu\u00e7\u00e3o cl\u00ednica e orientar ajustes terap\u00eauticos.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><\/p>\n\n\n\n<figure class=\"wp-block-image size-large\"><a href=\"https:\/\/eventos.atlasemhematologia.com.br\/listadeesperatimeblogatlas\"><img decoding=\"async\" width=\"1030\" height=\"276\" src=\"https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2026\/03\/BANNER-BLOG-ATLAS-1030x276.png\" alt=\"\" class=\"wp-image-17314\" srcset=\"https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2026\/03\/BANNER-BLOG-ATLAS-1030x276.png 1030w, https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2026\/03\/BANNER-BLOG-ATLAS-300x80.png 300w, https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2026\/03\/BANNER-BLOG-ATLAS-768x206.png 768w, https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2026\/03\/BANNER-BLOG-ATLAS-1536x411.png 1536w, https:\/\/atlasemhematologia.com.br\/blog\/wp-content\/uploads\/2026\/03\/BANNER-BLOG-ATLAS-2048x549.png 2048w\" sizes=\"(max-width: 1030px) 100vw, 1030px\" \/><\/a><\/figure>\n\n\n\n<hr class=\"wp-block-separator has-alpha-channel-opacity\"\/>\n\n\n\n<p class=\"wp-block-paragraph\"><strong>Refer\u00eancias:<\/strong><\/p>\n\n\n\n<p class=\"wp-block-paragraph\">SILVA, M. R. et al. Diagn\u00f3stico da leucemia mieloide cr\u00f4nica: o papel das novas t\u00e9cnicas de biologia molecular. <strong>Hematology, Transfusion and Cell Therapy<\/strong>, v. 45, p. S121, 2023.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Doen\u00e7as que alteram os exames hematol\u00f3gicos \/ Fl\u00e1vio Augusto Naoum. &#8211; 2. ed. &#8211; Rio de Janeiro: Atheneu, 2017<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">BOLLMANN, Patricia Weinschenker; GIGLIO, Auro del. Leucemia mieloide cr\u00f4nica: passado, presente, futuro. Einstein (S\u00e3o Paulo), v. 9, p. 236-243, 2011.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Swerdlow SH, Campo E, Harris NL, Jaffe ES, Pileri SA, Stein H, Thiele J, Vardiman JW. WHO Classification of Tumours of Haematopoietic and Lymphoid Tissues. Lyon: IARC Press; 2008.&nbsp;<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">SOSSELA, Fernanda Roberta; ZOPPAS, Barbara Catarina de Antoni; WEBER, Liliana Portal. Leucemia Mieloide Cr\u00f4nica: aspectos cl\u00ednicos, diagn\u00f3stico e principais altera\u00e7\u00f5es observadas no hemograma. RBAC, v. 49, n. 2, p. 127-30, 2017.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>A leucemia mieloide cr\u00f4nica (LMC) \u00e9 classificada como uma neoplasia mieloproliferativa e acomete principalmente adultos, com maior incid\u00eancia entre os 40 e 50 anos. Trata-se de uma doen\u00e7a hematopoi\u00e9tica clonal caracterizada por uma altera\u00e7\u00e3o citogen\u00e9tica espec\u00edfica, resultante da transloca\u00e7\u00e3o cromoss\u00f4mica t(9;22)(q34;q11), conhecida como cromossomo Philadelphia. Essa transloca\u00e7\u00e3o origina o gene de fus\u00e3o BCR-ABL1, respons\u00e1vel pela [&hellip;]<\/p>\n","protected":false},"author":6,"featured_media":17517,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"pagelayer_contact_templates":[],"_pagelayer_content":"","footnotes":""},"categories":[18],"tags":[],"class_list":["post-17515","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-doencas-hematologicas"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.2 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Leucemia Mieloide Cr\u00f4nica - Blog - Atlas em Hematologia<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/atlasemhematologia.com.br\/blog\/leucemia-mieloide-cronica\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Leucemia Mieloide Cr\u00f4nica - Blog - Atlas em Hematologia\" \/>\n<meta property=\"og:description\" content=\"A leucemia mieloide cr\u00f4nica (LMC) \u00e9 classificada como uma neoplasia mieloproliferativa e acomete principalmente adultos, com maior incid\u00eancia entre os 40 e 50 anos. Trata-se de uma doen\u00e7a hematopoi\u00e9tica clonal caracterizada por uma altera\u00e7\u00e3o citogen\u00e9tica espec\u00edfica, resultante da transloca\u00e7\u00e3o cromoss\u00f4mica t(9;22)(q34;q11), conhecida como cromossomo Philadelphia. 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